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Arrhythmia Testing
Table 1: Description of inherited arrhythmia conditions
Heart Rhythm Society (HRS) and European Heart Rhythm Association (EHRA) Consensus
Guidelines on Genetic Testing for Channelopathies: 19
Individuals with a Clinical Asymptomatic
Disorder Relatives (Familial
Diagnosis
Mutation Testing)
LQTS Class I Class I
CPVT Class I Class I Recommendation Classes
Class I: Genetic testing is recommended. Test result impacts
BrS Class IIa Class I diagnosis and/or management recommendations.
Class IIa: Genetic testing can be useful for patients with a
SQTS Class IIb Class I
clinical diagnosis.
Class IIa Class IIb: Genetic testing may be considered as part of the
ARVC (For patients meeting the ARVC task Class I diagnostic evaluation.
force diagnostice criteria) Class III: Genetic testing is not recommended.
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