Page 177 - Biochemistry PharmD General
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Type-III (Limit dextrinosis)
[Frobe’s Disease or Cori’s Disease]
• It is caused by deficiency of debranching enzyme
(during glycogenolysis).
• This results in the accumulation of abnormal type of
glycogen (i.e. trimmed glycogen) with short branches
almost looks like the structure of limit dextrin
molecule.
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