Page 178 - Biochemistry PharmD General
P. 178

Type IV (Amylopectinosis);
                         Andersen’s Disease

• Is caused by deficiency of branching enzyme (during
   glycogenesis).

• Glycogen formed has few branches like amylopectin.
• Death of cardiac or liver failure usually in the first

   year of life.

                                                                                                                                   177
   173   174   175   176   177   178   179   180   181   182   183